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<ciselnik xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xsi:noNamespaceSchemaLocation="https://ciselniky.dasta.mzcr.cz/xmlschema/uzis-4.13.07.xsd" nazev="DgSsiem" zkratka="-" spravce="uzis" dat_gen="2017-11-24" cas_gen="10:00:00" ver_nclp="02.97.01" ver_ds="04.28.05" cis_klic="kod" uzis_verze="202620" u_plati_od="2026-05-01" popis="Číselník použitý v NRVV">
  <VETA kod="1.               " popis="Disorders of amino acid and peptide metabolism" plati_od="2016-01-01" />
  <VETA kod="1.1.             " popis="Urea cycle disorders and inherited hyperammonaemias" plati_od="2016-01-01" />
  <VETA kod="1.1.0.           " popis="Other disorders of the urea cycle" plati_od="2016-01-01" />
  <VETA kod="1.1.1.           " popis="Carbamoylphosphate synthetase I deficiency" plati_od="2016-01-01" />
  <VETA kod="1.1.2.           " popis="N-Acetylglutamate synthetase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.1.3.           " popis="Ornithine transcarbamylase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.1.4.           " popis="Citrullinemia type 1" plati_od="2016-01-01" />
  <VETA kod="1.1.5.           " popis="Argininosuccinic aciduria" plati_od="2016-01-01" />
  <VETA kod="1.1.6.           " popis="Argininemia" plati_od="2016-01-01" />
  <VETA kod="1.1.7.           " popis="HHH syndrome" plati_od="2016-01-01" />
  <VETA kod="1.1.8.           " popis="Citrullinemia type 2" plati_od="2016-01-01" />
  <VETA kod="1.1.9.           " popis="Hyperinsulinemic hypoglycemia and hyperammonemia caused by activating mutations in the GLUD1 gene" plati_od="2016-01-01" />
  <VETA kod="1.2.             " popis="Organic acidurias" plati_od="2016-01-01" />
  <VETA kod="1.2.1.           " popis="Glutaric aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.1.1.         " popis="Glutaric aciduria type 1" plati_od="2016-01-01" />
  <VETA kod="1.2.1.2.         " popis="Glutaric aciduria type 3" plati_od="2016-01-01" />
  <VETA kod="1.2.2.           " popis="Propionic aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.3.           " popis="Methylmalonic aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.3.1.         " popis="Methylmalonyl-CoA mutase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.2.3.2.         " popis="Methylmalonyl-CoA epimerase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.2.3.3.         " popis="Methylmalonic aciduria, unspecified" plati_od="2016-01-01" />
  <VETA kod="1.2.4.           " popis="Isovaleric aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.5.           " popis="Methylcrotonylglycinuria" plati_od="2016-01-01" />
  <VETA kod="1.2.6.           " popis="Methylglutaconic aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.6.1.         " popis="Methylglutaconic aciduria type 1" plati_od="2016-01-01" />
  <VETA kod="1.2.6.2.         " popis="3-methylglutaconic aciduria type 2" plati_od="2016-01-01" />
  <VETA kod="1.2.6.3.         " popis="3-methylglutaconic aciduria type 3" plati_od="2016-01-01" />
  <VETA kod="1.2.6.4.         " popis="3-methylglutaconic aciduria type 4" plati_od="2016-01-01" />
  <VETA kod="1.2.6.5.         " popis="3-methylglutaconic aciduria type 5" plati_od="2016-01-01" />
  <VETA kod="1.2.7.           " popis="3-hydroxy-3-methylglutaric aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.8.           " popis="2-methylbutyric aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.9.           " popis="2-Methyl-3-hydroxybutyric aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.10.          " popis="Alpha-methylacetoacetic aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.11.          " popis="Isobutyric aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.12.          " popis="Methacrylic aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.13.          " popis="3-hydroxyisobutyric aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.14.          " popis="Methylmalonate semialdehyde dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.2.15.          " popis="L-2-hydroxyglutaric aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.16.          " popis="D-2-hydroxyglutaric aciduria" plati_od="2016-01-01" />
  <VETA kod="1.2.16.1.        " popis="D-2-hydroxyglutarate dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.2.16.2.        " popis="Mitochondrial isocitrate dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.2.17.          " popis="Aminoacylase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.2.17.1.        " popis="Aminoacylase 1 deficiency" plati_od="2016-01-01" />
  <VETA kod="1.2.17.2.        " popis="Aminoacylase 2 deficiency" plati_od="2016-01-01" />
  <VETA kod="1.2.18.          " popis="Methylmalonate semialdehyde dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.2.0.           " popis="Other organic acidurias" plati_od="2016-01-01" />
  <VETA kod="1.3.             " popis="Disorders of the metabolism of branched-chain amino acids not classified as organic acidurias" plati_od="2016-01-01" />
  <VETA kod="1.3.1.           " popis="Branched-chain amino acid transferase" plati_od="2016-01-01" />
  <VETA kod="1.3.2.           " popis="Maple syrup urine disease" plati_od="2016-01-01" />
  <VETA kod="1.3.2.1.         " popis="BCKD E1 alpha subunit of deficiency" plati_od="2016-01-01" />
  <VETA kod="1.3.2.2.         " popis="BCKD E1 beta subunit of deficiency" plati_od="2016-01-01" />
  <VETA kod="1.3.2.3.         " popis="Dihydrolipoamide branched chain transacylase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.3.2.4.         " popis="Unspecified BCKD deficiency" plati_od="2016-01-01" />
  <VETA kod="1.3.0.           " popis="Other disorders of branched-chain amino acid metabolism" plati_od="2016-01-01" />
  <VETA kod="1.4.             " popis="Disorders of phenylalanine or tyrosine metabolism" plati_od="2016-01-01" />
  <VETA kod="1.4.1.           " popis="Phenylalanine hydroxylase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.4.2.           " popis="Tyrosinemia type 2" plati_od="2016-01-01" />
  <VETA kod="1.4.3.           " popis="Tyrosinemia type 3" plati_od="2016-01-01" />
  <VETA kod="1.4.4.           " popis="Hawkinsinuria" plati_od="2016-01-01" />
  <VETA kod="1.4.5.           " popis="Alkaptonuria" plati_od="2016-01-01" />
  <VETA kod="1.4.6.           " popis="Tyrosinemia type 1" plati_od="2016-01-01" />
  <VETA kod="1.4.7.           " popis="Transient tyrosinaemia of the neonate" plati_od="2016-01-01" />
  <VETA kod="1.4.0.           " popis="Other disorders of phenylalanine or tyrosine metabolism" plati_od="2016-01-01" />
  <VETA kod="1.5.             " popis="Disorders of the metabolism of sulphur amino acids" plati_od="2016-01-01" />
  <VETA kod="1.5.1.           " popis="Methionine adenosyltransferase I/III deficiency" plati_od="2016-01-01" />
  <VETA kod="1.5.2.           " popis="Glycine N-methyltransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.5.3.           " popis="S-adenosylhomocysteine hydrolase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.5.4.           " popis="Cystathionine beta-synthase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.5.5.           " popis="Cystathionase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.5.6.           " popis="Isolated sulfite oxidase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.5.7.           " popis="Methionine synthase deficiency-cblG" plati_od="2016-01-01" />
  <VETA kod="1.5.8.           " popis="Methionine synthase reductase deficiency-cblE" plati_od="2016-01-01" />
  <VETA kod="1.5.0.           " popis="Other genetic defect in methionine cycle or sulfur amino acid metabolism" plati_od="2016-01-01" />
  <VETA kod="1.5.10.          " popis="Unspecified disorder of homocysteine metabolism" plati_od="2016-01-01" />
  <VETA kod="1.5.11.          " popis="Unspecified disorder of methionine metabolism" plati_od="2016-01-01" />
  <VETA kod="1.5.12.          " popis="Secondary non-genetic disorders of methionine cycle and other sulfur amino acids" plati_od="2016-01-01" />
  <VETA kod="1.6.             " popis="Disorders of histidine, tryptophan or lysine metabolism" plati_od="2016-01-01" />
  <VETA kod="1.6.1.           " popis="Histidinemia" plati_od="2016-01-01" />
  <VETA kod="1.6.2.           " popis="Urocanase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.6.3.           " popis="Glutamate formiminotransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.6.4.           " popis="Tryptophanaemia" plati_od="2016-01-01" />
  <VETA kod="1.6.5.           " popis="Hyperlysinaemia" plati_od="2016-01-01" />
  <VETA kod="1.6.5.1.         " popis="Hyperlysinaemia type I" plati_od="2016-01-01" />
  <VETA kod="1.6.5.2.         " popis="Hyperlysinaemia type II" plati_od="2016-01-01" />
  <VETA kod="1.6.6.           " popis="2-Aminoadipic aciduria" plati_od="2016-01-01" />
  <VETA kod="1.6.7.           " popis="2-Oxoadipic aciduria" plati_od="2016-01-01" />
  <VETA kod="1.6.8.           " popis="Hydroxykynureninuria" plati_od="2016-01-01" />
  <VETA kod="1.6.9.           " popis="Hydroxylysinuria" plati_od="2016-01-01" />
  <VETA kod="1.7.             " popis="Disorders of serine, glycine or glycerate metabolism" plati_od="2016-01-01" />
  <VETA kod="1.7.1.           " popis="Phosphoglycerate dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.7.2.           " popis="Phosphoserine phosphatase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.7.3.           " popis="Phosphoserine aminotransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.7.4.           " popis="Nonketotic hyperglycinaemia" plati_od="2016-01-01" />
  <VETA kod="1.7.4.1.         " popis="P protein deficiency, GLDC gene" plati_od="2016-01-01" />
  <VETA kod="1.7.4.2.         " popis="T protein deficiency, AMT gene" plati_od="2016-01-01" />
  <VETA kod="1.7.4.3.         " popis="H protein deficiency, GCSH gene" plati_od="2016-01-01" />
  <VETA kod="1.7.5.           " popis="Sarcosinemia" plati_od="2016-01-01" />
  <VETA kod="1.7.6.           " popis="D-glyceric aciduria" plati_od="2016-01-01" />
  <VETA kod="1.8.             " popis="Disorders of ornithine or proline metabolism" plati_od="2016-01-01" />
  <VETA kod="1.8.1.           " popis="Ornithine aminotransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.8.2.           " popis="Hyperprolinemia type 1" plati_od="2016-01-01" />
  <VETA kod="1.8.3.           " popis="Hyperprolinemia type 2" plati_od="2016-01-01" />
  <VETA kod="1.8.4.           " popis="Hypoprolinaemia" plati_od="2016-01-01" />
  <VETA kod="1.8.5.           " popis="Cutis laxa, autosomal recessive, type IIb" plati_od="2016-01-01" />
  <VETA kod="1.9.             " popis="Disorders of amino acid transport" plati_od="2016-01-01" />
  <VETA kod="1.9.1.           " popis="Lysinuric protein intolerance" plati_od="2016-01-01" />
  <VETA kod="1.9.2.           " popis="Cystinuria" plati_od="2016-01-01" />
  <VETA kod="1.9.3.           " popis="Cystinuria-hypotonia syndrome (contiguous gene defect)" plati_od="2016-01-01" />
  <VETA kod="1.9.4.           " popis="Hartnup disease" plati_od="2016-01-01" />
  <VETA kod="1.9.5.           " popis="Iminoglycinuria" plati_od="2016-01-01" />
  <VETA kod="1.9.6.           " popis="Lowe syndrome" plati_od="2016-01-01" />
  <VETA kod="1.9.0.           " popis="Other disorders of amino acid transport" plati_od="2016-01-01" />
  <VETA kod="1.10.            " popis="Other disorders of amino acid metabolism" plati_od="2016-01-01" />
  <VETA kod="1.10.1.          " popis="Glutamine synthetase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.11.            " popis="Disorders of the gamma-glutamyl cycle" plati_od="2016-01-01" />
  <VETA kod="1.11.1.          " popis="Glutathionuria" plati_od="2016-01-01" />
  <VETA kod="1.11.2.          " popis="Cysteinylglycinase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.11.3.          " popis="Oxoprolinuria" plati_od="2016-01-01" />
  <VETA kod="1.11.4.          " popis="Gamma-glutamylcysteine synthetase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.11.5.          " popis="Glutathione synthetase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.12.            " popis="Other disorders of peptide metabolism" plati_od="2016-01-01" />
  <VETA kod="1.12.1.          " popis="Prolidase deficiency" plati_od="2016-01-01" />
  <VETA kod="1.12.2.          " popis="Carnosinaemia" plati_od="2016-01-01" />
  <VETA kod="1.12.3.          " popis="Homocarnosinosis" plati_od="2016-01-01" />
  <VETA kod="1.13.            " popis="Other disorders of amino acid and protein metabolism" plati_od="2016-01-01" />
  <VETA kod="2.               " popis="Disorders of carbohydrate metabolism" plati_od="2016-01-01" />
  <VETA kod="2.1.             " popis="Disorders of galactose metabolism" plati_od="2016-01-01" />
  <VETA kod="2.1.1.           " popis="Classic galactosemia" plati_od="2016-01-01" />
  <VETA kod="2.1.2.           " popis="Galactokinase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.1.3.           " popis="Uridine diphosphate galactose-4-epimerase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.2.             " popis="Disorders of fructose metabolism" plati_od="2016-01-01" />
  <VETA kod="2.2.1.           " popis="Essential fructosuria" plati_od="2016-01-01" />
  <VETA kod="2.2.2.           " popis="Hereditary fructose intolerance" plati_od="2016-01-01" />
  <VETA kod="2.3.             " popis="Disorders of pentose metabolism" plati_od="2016-01-01" />
  <VETA kod="2.3.1.           " popis="Essential pentosuria" plati_od="2016-01-01" />
  <VETA kod="2.3.2.           " popis="Ribose-5-phosphate isomerase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.3.3.           " popis="Transaldolase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.4.             " popis="Disorders of glycerol metabolism" plati_od="2016-01-01" />
  <VETA kod="2.4.1.           " popis="Glycerol kinase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.4.2.           " popis="Complex glycerol kinase deficiency due to contiguous gene deletion" plati_od="2016-01-01" />
  <VETA kod="2.5.             " popis="Disorders of glyoxylate metabolism" plati_od="2016-01-01" />
  <VETA kod="2.5.1.           " popis="Primary hyperoxaluria type I" plati_od="2016-01-01" />
  <VETA kod="2.5.2.           " popis="Primary hyperoxaluria type II" plati_od="2016-01-01" />
  <VETA kod="2.6.             " popis="Disorders of glucose transport" plati_od="2016-01-01" />
  <VETA kod="2.6.1.           " popis="Glucose transporter 1 deficiency (blood-brain barrier)" plati_od="2016-01-01" />
  <VETA kod="2.6.2.           " popis="Glucose transporter 2 deficiency" plati_od="2016-01-01" />
  <VETA kod="2.6.3.           " popis="Glucose/galactose malabsorption" plati_od="2016-01-01" />
  <VETA kod="2.7.             " popis="Disorders of gluconeogenesis" plati_od="2016-01-01" />
  <VETA kod="2.7.1.           " popis="Fructose-1,6-bisphosphatase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.7.2.           " popis="Pyruvate carboxylase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.7.3.           " popis="Phosphoenolpyruvate carboxykinase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.8.             " popis="Glycogen storage disorders" plati_od="2016-01-01" />
  <VETA kod="2.8.1.           " popis="Glycogen storage disease type 1a" plati_od="2016-01-01" />
  <VETA kod="2.8.2.           " popis="Glycogen storage disease type 1b" plati_od="2016-01-01" />
  <VETA kod="2.8.3.           " popis="Glycogen storage disease type II" plati_od="2016-01-01" />
  <VETA kod="2.8.4.           " popis="Glycogen storage disease type III" plati_od="2016-01-01" />
  <VETA kod="2.8.5.           " popis="Glycogen storage disease type IV" plati_od="2016-01-01" />
  <VETA kod="2.8.6.           " popis="Glycogen storage disease type V" plati_od="2016-01-01" />
  <VETA kod="2.8.7.           " popis="Glycogen storage disease type VI" plati_od="2016-01-01" />
  <VETA kod="2.8.8.           " popis="Glycogen storage disease type VII" plati_od="2016-01-01" />
  <VETA kod="2.8.9.           " popis="Glycogen storage disease type IX" plati_od="2016-01-01" />
  <VETA kod="2.8.9.1.         " popis="Hepatic phosphorylase kinase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.8.9.2.         " popis="Hepatic and muscle phosphorylase kinase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.8.9.3.         " popis="Muscle phosphorylase kinase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.8.9.4.         " popis="Cardiac muscle phosphorylase kinase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.8.10.          " popis="Glycogen storage disease type X" plati_od="2016-01-01" />
  <VETA kod="2.8.11.          " popis="Glycogen storage disease type XI" plati_od="2016-01-01" />
  <VETA kod="2.8.12.          " popis="Glycogen storage disease type XIV" plati_od="2016-01-01" />
  <VETA kod="2.8.13.          " popis="Glycogen storage disease type XV" plati_od="2016-01-01" />
  <VETA kod="2.8.14.          " popis="Glycogen storage disease type 0a" plati_od="2016-01-01" />
  <VETA kod="2.8.15.          " popis="Glycogen storage disease type 0b" plati_od="2016-01-01" />
  <VETA kod="2.8.16.          " popis="Other glycogen storage disease" plati_od="2016-01-01" />
  <VETA kod="2.8.16.1.        " popis="Muscle LDH deficiency" plati_od="2016-01-01" />
  <VETA kod="2.8.16.2.        " popis="Aldolase A deficiency" plati_od="2016-01-01" />
  <VETA kod="2.8.16.3.        " popis="Beta-enolase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.8.16.4.        " popis="Muscle phosphoglycerate kinase deficiency" plati_od="2016-01-01" />
  <VETA kod="2.8.17.          " popis="Unspecified glycogen storage disease" plati_od="2016-01-01" />
  <VETA kod="2.9.             " popis="Other carbohydrate disorders" plati_od="2016-01-01" />
  <VETA kod="2.9.1.           " popis="Lactose intolerance" plati_od="2016-01-01" />
  <VETA kod="2.9.2.           " popis="Disaccharide intolerance 1" plati_od="2016-01-01" />
  <VETA kod="2.9.3.           " popis="Trehalase deficiency" plati_od="2016-01-01" />
  <VETA kod="3.               " popis="Disorders of fatty acid and ketone body metabolism" plati_od="2016-01-01" />
  <VETA kod="3.1.             " popis="Disorders of lipolysis" plati_od="2016-01-01" />
  <VETA kod="3.2.             " popis="Disorders of carnitine transport and the carnitine cycle" plati_od="2016-01-01" />
  <VETA kod="3.2.1.           " popis="Carnitine transporter deficiency" plati_od="2016-01-01" />
  <VETA kod="3.2.2.           " popis="Carnitine palmitoyltransferase I (CPTI) deficiency" plati_od="2016-01-01" />
  <VETA kod="3.2.3.           " popis="Carnitine acylcarnitine translocase deficiency" plati_od="2016-01-01" />
  <VETA kod="3.2.4.           " popis="Carnitine palmitoyltransferase II (CPTII) deficiency" plati_od="2016-01-01" />
  <VETA kod="3.3.             " popis="Disorders of mitochondrial fatty acid oxidation" plati_od="2016-01-01" />
  <VETA kod="3.3.1.           " popis="Very long - chain acyl CoA dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="3.3.2.           " popis="Mitochondrial trifunctional protein deficiency" plati_od="2016-01-01" />
  <VETA kod="3.3.2.1.         " popis="Isolated deficiency of long-chain 3-hydroxyacyl-CoA dehydrogenase" plati_od="2016-01-01" />
  <VETA kod="3.3.2.2.         " popis="Isolated deficiency of long-chain 3-ketoacyl CoA thiolase" plati_od="2016-01-01" />
  <VETA kod="3.3.3.           " popis="Medium - chain acyl CoA dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="3.3.4.           " popis="Short - chain acyl CoA dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="3.3.5.           " popis="3-alpha-hydroxyacyl- CoA dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="3.3.6.           " popis="Multiple acyl-CoA dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="3.3.6.1.         " popis="Electron transfer flavoprotein deficiency, alpha chain" plati_od="2016-01-01" />
  <VETA kod="3.3.6.2.         " popis="Electron transfer flavoprotein deficiency, beta chain" plati_od="2016-01-01" />
  <VETA kod="3.3.6.3.         " popis="ETF-ubiquinone oxidoreductase deficiency" plati_od="2016-01-01" />
  <VETA kod="3.4.             " popis="Disorders of ketone body metabolism" plati_od="2016-01-01" />
  <VETA kod="3.4.1.           " popis="3-Hydroxy-3-Methylglutaryl-CoA synthase deficieny" plati_od="2016-01-01" />
  <VETA kod="3.4.2.           " popis="Succinyl-CoA:3-Oxoacid-CoA transferase (SCOT) deficiency" plati_od="2016-01-01" />
  <VETA kod="3.4.3.           " popis="Cytosolic acetoacetyl-CoA thiolase deficiency" plati_od="2016-01-01" />
  <VETA kod="3.5.             " popis="Other disorders of fatty acid and ketone body metabolism" plati_od="2016-01-01" />
  <VETA kod="3.5.1.           " popis="Long - chain acyl CoA dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="3.5.2.           " popis="Malonyl CoA decarboxylase deficiency" plati_od="2016-01-01" />
  <VETA kod="4.               " popis="Disorders of energy metabolism" plati_od="2016-01-01" />
  <VETA kod="4.1.             " popis="Disorders of pyruvate metabolism" plati_od="2016-01-01" />
  <VETA kod="4.1.1.           " popis="Pyruvate dehydrogenase complex deficiency" plati_od="2016-01-01" />
  <VETA kod="4.1.1.1.         " popis="Pyruvate dehydrogenase E1? subunit deficiency" plati_od="2016-01-01" />
  <VETA kod="4.1.1.2.         " popis="Pyruvate dehydrogenase E1ß subunit deficiency" plati_od="2016-01-01" />
  <VETA kod="4.1.1.3.         " popis="Dihydrolipoyl transacetylase deficiency" plati_od="2016-01-01" />
  <VETA kod="4.1.1.4.         " popis="Dihydrolipoyl dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="4.1.1.5.         " popis="Pyruvate dehydrogenase E3 binding protein deficiency" plati_od="2016-01-01" />
  <VETA kod="4.1.1.6.         " popis="Pyruvate dehydrogenase phosphatase deficiency" plati_od="2016-01-01" />
  <VETA kod="4.1.1.7.         " popis="Pyruvate dehydrogenase deficiency, unspecified" plati_od="2016-01-01" />
  <VETA kod="4.1.2.           " popis="Pyruvate kinase deficiency" plati_od="2016-01-01" />
  <VETA kod="4.2.             " popis="Disorders of the citric acid cycle" plati_od="2016-01-01" />
  <VETA kod="4.2.1.           " popis="2-Oxoglutarate dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="4.2.2.           " popis="Fumarase deficiency" plati_od="2016-01-01" />
  <VETA kod="4.3.             " popis="Mitochondrial respiratory chain disorders" plati_od="2016-01-01" />
  <VETA kod="4.3.1.           " popis="Respiratory chain disorders caused by mutations of mtDNA" plati_od="2016-01-01" />
  <VETA kod="4.3.1.1.         " popis="Large-scale single deletion of mtDNA" plati_od="2016-01-01" />
  <VETA kod="4.3.1.1.1.       " popis="Pearson Syndrome" plati_od="2016-01-01" />
  <VETA kod="4.3.1.1.2.       " popis="Kearns Sayre Syndrome" plati_od="2016-01-01" />
  <VETA kod="4.3.1.1.3.       " popis="Chronic Progressive External Ophthalmoplegia (CPEO) with Mitochondrial Myopathy [onset after 20 yrs]" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.         " popis="Point mutations of mtDNA" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.1.       " popis="Mitochondrial encephalomyopathy lactic acidosis and stroke-like episodes, MELAS" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.2.       " popis="Myoclonic epilepsy associated with ragged red fibres, MERRF" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.3.       " popis="Neuropathy Ataxia and Retinitis Pigmentosa, NARP" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.4.       " popis="Leber Hereditary Optic Neuropathy, LHON" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.5.       " popis="Maternally Inherited Leigh Syndrome, MILS" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.6.       " popis="Sporadic Leigh Syndrome" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.7.       " popis="Maternally inherited Mitochondrial Dystonia" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.8.       " popis="Maternally inherited Mitochondrial Cardiomyopathy" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.9.       " popis="Maternally inherited Mitochondrial Myopathy" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.9.1.     " popis="‘Pure’ Mitochondrial Myopathy" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.9.2.     " popis="Lethal Infantile Mitochondrial Myopathy" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.9.3.     " popis="Mitochondrial Myopathy with Diabetes Mellitus" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.9.4.     " popis="Mitochondrial Myopathy with Reversible cytochrome c oxidase (COX) Deficiency" plati_od="2016-01-01" />
  <VETA kod="4.3.1.2.10.      " popis="Maternally inherited deafness and diabetes, MIDD" plati_od="2016-01-01" />
  <VETA kod="4.3.2.           " popis="Respiratory chain disorders caused by mutations of nuclear DNA" plati_od="2016-01-01" />
  <VETA kod="4.3.2.1.         " popis="Mitochondrial DNA Depletion Syndromes" plati_od="2016-01-01" />
  <VETA kod="4.3.2.1.1.       " popis="Alpers-Huttenlocher Syndrome (POLG)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.1.2.       " popis="Hepatocerebral (DGUOK, MPV17, PEO1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.1.3.       " popis="Myopathic (TK2)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.1.4.       " popis="Encephalomyopathy with methylmalonic aciduria (SUCLA2)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.1.5.       " popis="Fatal Infantile Lactic Acidosis with methylmalonic aciduria (SUCLG1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.1.6.       " popis="Encephalomyopathic with renal tubulopathy (RRM2B)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.1.7.       " popis="Childhood-onset autosomal dominant optic atophy (OPA1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.1.8.       " popis="Mitochondrial Neurogastrointestinal Encephalopathy, MNGIE (ECGF1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.2.         " popis="Multiple mtDNA Deletion Syndromes" plati_od="2016-01-01" />
  <VETA kod="4.3.2.2.1.       " popis="Progressive External Ophthalmoplegia Autosomal Dominant (PEOA)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.2.1.1.     " popis="PEOA1 (POLG)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.2.1.2.     " popis="PEOA2 (ANT1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.2.1.3.     " popis="PEOA3 (PEO1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.2.1.4.     " popis="PEOA4 (POLG2)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.2.1.5.     " popis="PEOA5 (RRM2B)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.2.2.       " popis="Progressive External Ophthalmoplegia Autosomal Recessive (PEOB)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.2.3.       " popis="Sensory Ataxic Neuropathy, Dysarthria and Ophthalmoparesis, SANDO" plati_od="2016-01-01" />
  <VETA kod="4.3.2.2.4.       " popis="Optic Atrophy 1 and Deafness (OPA1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.3.         " popis="Leigh Syndrome, LS" plati_od="2016-01-01" />
  <VETA kod="4.3.2.3.1.       " popis="LS with leukodystrophy (SDHA, SURF1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.3.2.       " popis="LS with cardiomyopathy (COX10, COX15)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.3.3.       " popis="LS with French-Canadian ethnicity (LRPPRC)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.3.4.       " popis="LS with nephrotic syndrome (PDSS2)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.3.5.       " popis="LS with nephropathy (COQ2)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.4.         " popis="Ubiquinone (CoQ10) deficiency (Non-LS)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.4.1.       " popis="Early-onset ataxia with oculomotor apraxia and hypoalbuminaemia (APTX)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.4.2.       " popis="Deafness, encephaloneuropathy, obesity and valvulopathy (PDSS1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.4.3.       " popis="Cerebellar atrophy, ataxia and seizures (CABC1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.5.         " popis="Growth Retardation, Aminoaciduria, Cholestasis, Iron overload, Lactic acidosis and Early death (GRACILE) Syndrome (BCS1L)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.6.         " popis="Renal tubulopathy, encephalopathy and liver failure (BCS1L)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.7.         " popis="Cardio-encephalopathy with hyperammonaemia (TMEM70)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.8.         " popis="Exercise Intolerance with Lactic Acidosis" plati_od="2016-01-01" />
  <VETA kod="4.3.2.8.1.       " popis="Complex I deficiency; riboflavin responsive (ACAD9)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.8.2.       " popis="Complex I and II deficiency (ISCU)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.9.         " popis="Isolated Oxidative Phosphorylation Defects with Variable Phenotype (Not Classified Elsewhere)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.9.1.       " popis="Complex I structural subunit gene defect (NDUFV1, NDUFV2, NDUFS1, NDUFS2, NDUFS3, NDUFS4, NDUFS6, NDUFS7, NDUFS8, NDUFA1, NDUFA2, NDUFA11)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.9.2.       " popis="Complex I assembly gene defect (C20orf7, NDUFAF1, NDUFAF2, NDUFAF3, NDUFAF4, C80orf38, NUBPL, FOXRED1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.9.3.       " popis="Complex II structural subunit gene defect (SDHA, SDHB, SDHC, SDHD)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.9.4.       " popis="Complex II assembly gene defect (SDHAF1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.9.5.       " popis="Complex III structural subunit gene defect (UQCRB, UQCRQ)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.9.6.       " popis="Complex III assembly gene defect" plati_od="2016-01-01" />
  <VETA kod="4.3.2.9.7.       " popis="Complex IV structural subunit gene defect (COX6B1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.9.8.       " popis="Complex IV assembly gene defect (SCO1, SCO2, SURF1, COX10, COX15, TACO1, FASTKD2)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.9.9.       " popis="Complex V structural subunit gene defect (ATP5E)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.9.10.      " popis="Complex V assembly gene defect (ATPAF2, TMEM70)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.        " popis="Mitochondrial Protein Translation Defects" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.1.      " popis="Combined Oxidative Phosphorylation Defect 1, COXPD1 (EFG1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.2.      " popis="Combined Oxidative Phosphorylation Defect 2, COXPD2 (MRPS16)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.3.      " popis="Combined Oxidative Phosphorylation Defect 3, COXPD3 (TSFM)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.4.      " popis="Combined Oxidative Phosphorylation Defect 4, COXPD4 (TUFM)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.5.      " popis="Combined Oxidative Phosphorylation Defect 5, COXPD5 (MRPS22)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.6.      " popis="Combined Oxidative Phosphorylation Defect 6, COXPD6 (AIFM1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.7.      " popis="Combined Oxidative Phosphorylation Defect 7, COXPD7 (C10ORF65)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.8.      " popis="Myopathy, Lactic Acidosis and Sideroblastic Anaemia 1, MLASA1 (PUS1)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.9.      " popis="Acute Infantile Liver Failure (TRMU)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.10.     " popis="Leukoencephalopathy with brainstem and spinal cord involvement and lactate elevation, LBSL (DARS2)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.11.     " popis="Pontocerebellar hypoplasia Type 6 (RARS2)" plati_od="2016-01-01" />
  <VETA kod="4.3.2.10.12.     " popis="Myopathy, Lactic Acidosis and Sideroblastic Anaemia 2, MLASA2 (YARS2)" plati_od="2016-01-01" />
  <VETA kod="4.3.3.           " popis="Respiratory chain deficiencies with no known genetic basis" plati_od="2016-01-01" />
  <VETA kod="4.3.3.1.         " popis="Complex I deficiency" plati_od="2016-01-01" />
  <VETA kod="4.3.3.2.         " popis="Complex II deficiency" plati_od="2016-01-01" />
  <VETA kod="4.3.3.3.         " popis="Complex III deficiency" plati_od="2016-01-01" />
  <VETA kod="4.3.3.4.         " popis="Complex IV deficiency" plati_od="2016-01-01" />
  <VETA kod="4.3.3.5.         " popis="ATP synthase deficiency" plati_od="2016-01-01" />
  <VETA kod="4.3.3.6.         " popis="Combined respiratory chain deficiency" plati_od="2016-01-01" />
  <VETA kod="4.4.             " popis="Mitochondrial membrane transport disorders" plati_od="2016-01-01" />
  <VETA kod="4.4.1.           " popis="Mitochondrial substrate carrier disorders" plati_od="2016-01-01" />
  <VETA kod="4.4.1.1.         " popis="Mitochondrial phosphate carrier deficiency (SLC25A3)" plati_od="2016-01-01" />
  <VETA kod="4.4.1.2.         " popis="Mitochondrial aspartate glutamate carrier 1 deficiency (SLC25A12)" plati_od="2016-01-01" />
  <VETA kod="4.4.1.3.         " popis="Mitochondrial glutamate carrier 1 deficiency (SLC25A22)" plati_od="2016-01-01" />
  <VETA kod="4.4.1.4.         " popis="Mitochondrial carrier SLC25A38, haem biosynthesis, sideroblastic anaemia" plati_od="2016-01-01" />
  <VETA kod="4.4.2.           " popis="Mitochondrial protein import disorders" plati_od="2016-01-01" />
  <VETA kod="4.4.2.1.         " popis="Mohr-Tranebjaerg syndrome (TIMM8A)" plati_od="2016-01-01" />
  <VETA kod="4.5.             " popis="Unspecified mitochondrial disorders" plati_od="2016-01-01" />
  <VETA kod="4.5.1.           " popis="Leigh syndrome with no known genetic or respiratory chain deficiency" plati_od="2016-01-01" />
  <VETA kod="4.5.2.           " popis="Ethylmalonic Encephalopathy (ETHE1)" plati_od="2016-01-01" />
  <VETA kod="4.5.3.           " popis="Anaemia, sideroblastic, and spinocerebellar ataxia, ASAT (ABCB7)" plati_od="2016-01-01" />
  <VETA kod="4.6.             " popis="Disorders of creatine metabolism" plati_od="2016-01-01" />
  <VETA kod="4.6.1.           " popis="Creatine transporter deficiency" plati_od="2016-01-01" />
  <VETA kod="4.6.2.           " popis="Guanidinoacetate methyltransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="4.6.3.           " popis="Arginine:glycine amidinotransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="4.7.             " popis="Other disorders of energy metabolism" plati_od="2016-01-01" />
  <VETA kod="5.               " popis="Disorders in the metabolism of purines, pyrimidines and nucleotides" plati_od="2016-01-01" />
  <VETA kod="5.1.             " popis="Disorders of purine metabolism" plati_od="2016-01-01" />
  <VETA kod="5.1.1.           " popis="Primary idiopathic gout" plati_od="2016-01-01" />
  <VETA kod="5.1.2.           " popis="Familial juvenile hyperuricaemic nephropathy" plati_od="2016-01-01" />
  <VETA kod="5.1.3.           " popis="Adenylosuccinate lyase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.1.4.           " popis="AICAR transformylase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.1.5.           " popis="Adenosine deaminase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.1.6.           " popis="Deoxyguanosine kinase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.1.7.           " popis="Myoadenylate deaminase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.1.8.           " popis="Lesch-Nyhan syndrome" plati_od="2016-01-01" />
  <VETA kod="5.1.9.           " popis="Adenine phosphoribosyl transferase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.1.10.          " popis="Phosphoribosyl pyrophosphate synthetase 1 defects" plati_od="2016-01-01" />
  <VETA kod="5.1.10.1.        " popis="Phosphoribosyl pyrophosphate synthase superactivity" plati_od="2016-01-01" />
  <VETA kod="5.1.10.2.        " popis="X-linked Charcot-Marie-Tooth disease-5" plati_od="2016-01-01" />
  <VETA kod="5.1.10.3.        " popis="Arts syndrome" plati_od="2016-01-01" />
  <VETA kod="5.1.10.4.        " popis="X-linked sensorineural deafness" plati_od="2016-01-01" />
  <VETA kod="5.1.11.          " popis="Inosine triphosphatase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.1.12.          " popis="Adenosine deaminase superactivity" plati_od="2016-01-01" />
  <VETA kod="5.1.13.          " popis="Purine nucleoside phosphorylase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.1.14.          " popis="Mitochondrial Ribonucelotide Reductase subunit 2 deficiency" plati_od="2016-01-01" />
  <VETA kod="5.1.15.          " popis="Xanthinuria type I" plati_od="2016-01-01" />
  <VETA kod="5.1.16.          " popis="Xanthinuria type II" plati_od="2016-01-01" />
  <VETA kod="5.1.17.          " popis="Thiopurine S-methyltransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.2.             " popis="Disorders of pyrimidine metabolism" plati_od="2016-01-01" />
  <VETA kod="5.2.1.           " popis="Orotic aciduria type I" plati_od="2016-01-01" />
  <VETA kod="5.2.2.           " popis="Orotic aciduria type II" plati_od="2016-01-01" />
  <VETA kod="5.2.3.           " popis="Pyrimidine - 5 - nucleotidase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.2.4.           " popis="Dihydroorotate dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.2.5.           " popis="Uridine-5’-monophosphate hydrolase superactivity" plati_od="2016-01-01" />
  <VETA kod="5.2.6.           " popis="Thymidine phosphorylase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.2.7.           " popis="Thymidine kinase 2 deficiency" plati_od="2016-01-01" />
  <VETA kod="5.2.8.           " popis="Dihydropyrimidine dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.2.9.           " popis="Dihydropyrimidinase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.2.10.          " popis="Beta-ureidopropionase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.2.11.          " popis="Hyper-beta-alaninaemia" plati_od="2016-01-01" />
  <VETA kod="5.2.12.          " popis="Beta-aminoisobutyrate-pyruvate transaminase deficiency" plati_od="2016-01-01" />
  <VETA kod="5.3.             " popis="Disorders of nucleotide metabolism" plati_od="2016-01-01" />
  <VETA kod="5.3.1.           " popis="Aicardi-Goutieres Syndrome (AGS)" plati_od="2016-01-01" />
  <VETA kod="5.3.1.1.         " popis="AGS1" plati_od="2016-01-01" />
  <VETA kod="5.3.1.2.         " popis="AGS2" plati_od="2016-01-01" />
  <VETA kod="5.3.1.3.         " popis="AGS3" plati_od="2016-01-01" />
  <VETA kod="5.3.1.4.         " popis="AGS4" plati_od="2016-01-01" />
  <VETA kod="5.3.1.5.         " popis="AGS5" plati_od="2016-01-01" />
  <VETA kod="5.3.2.           " popis="RNASET2-deficient cystic leukoencephalopathy" plati_od="2016-01-01" />
  <VETA kod="6.               " popis="Disorders of the metabolism of sterols" plati_od="2016-01-01" />
  <VETA kod="6.1.             " popis="Disorders of sterol biosynthesis" plati_od="2016-01-01" />
  <VETA kod="6.1.1.           " popis="Mevalonate kinase deficiency" plati_od="2016-01-01" />
  <VETA kod="6.1.2.           " popis="Smith - Lemli - Opitz syndrome" plati_od="2016-01-01" />
  <VETA kod="6.1.3.           " popis="X-linked dominant chondrodysplasia punctata 2" plati_od="2016-01-01" />
  <VETA kod="6.1.4.           " popis="Congenital hemidysplasia with ichtyosiform erythroderma and limb defects" plati_od="2016-01-01" />
  <VETA kod="6.1.5.           " popis="Desmosterolosis" plati_od="2016-01-01" />
  <VETA kod="6.1.6.           " popis="Lathosterolosis" plati_od="2016-01-01" />
  <VETA kod="6.1.7.           " popis="Greenberg skeletal dysplasia" plati_od="2016-01-01" />
  <VETA kod="6.2.             " popis="Disorders of bile acid biosynthesis" plati_od="2016-01-01" />
  <VETA kod="6.2.1.           " popis="3- ß-hydroxysterol  ?5-oxidoreductase/isomerase deficiency" plati_od="2016-01-01" />
  <VETA kod="6.2.2.           " popis="?4-3-oxysterol 5ß-reductase deficiency" plati_od="2016-01-01" />
  <VETA kod="6.2.3.           " popis="Oxysterol 7-alpha-hydroxylase" plati_od="2016-01-01" />
  <VETA kod="6.2.4.           " popis="Cholesterol 7-alpha-hydroxylase" plati_od="2016-01-01" />
  <VETA kod="6.2.5.           " popis="Cerebrotendinous xanthomatosis" plati_od="2016-01-01" />
  <VETA kod="6.3.             " popis="Disorders of bile acid metabolism and transport" plati_od="2016-01-01" />
  <VETA kod="6.3.1.           " popis="Bilirubin UDP-glucuronosyltransferase 1 deficiency" plati_od="2016-01-01" />
  <VETA kod="6.3.2.           " popis="Byler disease" plati_od="2016-01-01" />
  <VETA kod="6.3.3.           " popis="Progressive familial intrahepatic cholestasis type 2" plati_od="2016-01-01" />
  <VETA kod="6.3.4.           " popis="Progressive familial intrahepatic cholestasis type 3" plati_od="2016-01-01" />
  <VETA kod="6.4.             " popis="Other disorders in the metabolism of sterols" plati_od="2016-01-01" />
  <VETA kod="6.4.1.           " popis="X-linked ichthyosis" plati_od="2016-01-01" />
  <VETA kod="7.               " popis="Disorders of porphyrin and haem metabolism" plati_od="2016-01-01" />
  <VETA kod="7.1.1.           " popis="Erythropoietic porphyria" plati_od="2016-01-01" />
  <VETA kod="7.1.2.           " popis="X-linked dominant protoporphyria" plati_od="2016-01-01" />
  <VETA kod="7.1.3.           " popis="Variegate porphyria" plati_od="2016-01-01" />
  <VETA kod="7.1.4.           " popis="X-linked sideroblastic anaemia (XLSA)" plati_od="2016-01-01" />
  <VETA kod="7.1.5.           " popis="Congenital erythropoietic porphyria" plati_od="2016-01-01" />
  <VETA kod="7.1.6.           " popis="Acute intermittent porphyria" plati_od="2016-01-01" />
  <VETA kod="7.1.7.           " popis="Hereditary coproporphyria" plati_od="2016-01-01" />
  <VETA kod="7.1.8.           " popis="Porphyria cutanea tarda type I (sporadic)" plati_od="2016-01-01" />
  <VETA kod="7.1.9.           " popis="Porphyria cutanea tarda type II (familial)" plati_od="2016-01-01" />
  <VETA kod="7.1.10.          " popis="Acute hepatic porphyria" plati_od="2016-01-01" />
  <VETA kod="8.               " popis="Disorders of lipid and lipoprotein metabolism" plati_od="2016-01-01" />
  <VETA kod="8.1.             " popis="Inherited hypercholesterolaemias" plati_od="2016-01-01" />
  <VETA kod="8.1.1.           " popis="Disorder of low density lipoprotein receptor" plati_od="2016-01-01" />
  <VETA kod="8.1.1.1.         " popis="Familial hypercholesterolaemia - homozygous" plati_od="2016-01-01" />
  <VETA kod="8.1.1.2.         " popis="Familial hypercholesterolaemia - heterozygous" plati_od="2016-01-01" />
  <VETA kod="8.1.2.           " popis="Sitosterolaemia" plati_od="2016-01-01" />
  <VETA kod="8.2.             " popis="Inherited hypertriglyceridaemias" plati_od="2016-01-01" />
  <VETA kod="8.2.1.           " popis="Familial chylomicronaemia" plati_od="2016-01-01" />
  <VETA kod="8.2.1.1.         " popis="Familial lipoprotein lipase deficiency" plati_od="2016-01-01" />
  <VETA kod="8.2.1.2.         " popis="Familial apolipoprotein C - II deficiency" plati_od="2016-01-01" />
  <VETA kod="8.2.2.           " popis="Familial hypertriglyceridaemia" plati_od="2016-01-01" />
  <VETA kod="8.3.             " popis="Inherited mixed hyperlipidaemias" plati_od="2016-01-01" />
  <VETA kod="8.3.1.           " popis="Familial dysbetalipoproteinaemia" plati_od="2016-01-01" />
  <VETA kod="8.3.1.1.         " popis="Dysfunctional apo E" plati_od="2016-01-01" />
  <VETA kod="8.3.2.           " popis="Familial combined hyperlipoproteinaemia" plati_od="2016-01-01" />
  <VETA kod="8.3.3.           " popis="Hepatic lipase deficiency" plati_od="2016-01-01" />
  <VETA kod="8.4.             " popis="Disorders of high density lipoprotein metabolism" plati_od="2016-01-01" />
  <VETA kod="8.4.1.           " popis="Apolipoprotein A-I deficiency" plati_od="2016-01-01" />
  <VETA kod="8.4.2.           " popis="Tangier disease" plati_od="2016-01-01" />
  <VETA kod="8.4.3.           " popis="Lecithin cholesterol acyltransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="8.4.3.1.         " popis="Fish-eye disease" plati_od="2016-01-01" />
  <VETA kod="8.4.3.2.         " popis="Norum disease" plati_od="2016-01-01" />
  <VETA kod="8.4.4.           " popis="Familial hyperalphalipoproteinaemia" plati_od="2016-01-01" />
  <VETA kod="8.5.             " popis="Inherited hypolipidaemias" plati_od="2016-01-01" />
  <VETA kod="8.5.1.           " popis="Familial abetalipoproteinaemia" plati_od="2016-01-01" />
  <VETA kod="8.5.2.           " popis="Familial hypobetalipoproteinaemia" plati_od="2016-01-01" />
  <VETA kod="8.5.3.           " popis="Anderson disease" plati_od="2016-01-01" />
  <VETA kod="8.6.             " popis="Other disorders of lipid and lipoprotein metabolism" plati_od="2016-01-01" />
  <VETA kod="8.6.1.1.         " popis="Sjogren - Larsson syndrome" plati_od="2016-01-01" />
  <VETA kod="8.6.1.2.         " popis="Pancreatic triacylglycerol lipase deficiency" plati_od="2016-01-01" />
  <VETA kod="8.6.1.3.         " popis="Pancreatic colipase deficiency" plati_od="2016-01-01" />
  <VETA kod="8.7.             " popis="Unspecified disorders of lipid and lipoprotein metabolism" plati_od="2016-01-01" />
  <VETA kod="9.               " popis="Congenital disorders of glycosylation and other disorders of protein modification" plati_od="2016-01-01" />
  <VETA kod="9.1.             " popis="Disorders of protein N-glycosylation" plati_od="2016-01-01" />
  <VETA kod="9.1.1.           " popis="Phosphomannomutase 2 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.2.           " popis="Phosphomannose isomerase deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.3.           " popis="Glucosyltransferase 1 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.4.           " popis="Mannosyltransferase 6 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.5.           " popis="Mannosyltransferase 8 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.6.           " popis="Glucosyltransferase 2 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.7.           " popis="Mannosyltransferase 2 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.8.           " popis="UDP-GlcNAc:Dol-P-GlcNac-P transferase deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.9.           " popis="Mannosyltransferase 1 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.10.          " popis="Mannosyltransferase 7-9 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.11.          " popis="Flippase of Man5GlcNAc2-PP-Dol deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.12.          " popis="N-acetylglucosaminyltransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.13.          " popis="Glucosidase 1 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.1.14.          " popis="TUSC3-CDG" plati_od="2016-01-01" />
  <VETA kod="9.1.15.          " popis="SRD5A3-CDG" plati_od="2016-01-01" />
  <VETA kod="9.2.             " popis="Disorders of protein O-glycosylation" plati_od="2016-01-01" />
  <VETA kod="9.2.1.           " popis="O-xylosylglycan synthesis deficiencies" plati_od="2016-01-01" />
  <VETA kod="9.2.1.1.         " popis="EXT1 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.2.1.2.         " popis="EXT2 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.2.1.3.         " popis="Beta-1,4-galactosyltransferase 7 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.2.2.           " popis="O-N-acetylgalactosaminylglycan synthesis deficiencies" plati_od="2016-01-01" />
  <VETA kod="9.2.2.1.         " popis="Polypeptide N-acetylgalactosaminyl transferase deficiency" plati_od="2016-01-01" />
  <VETA kod="9.2.3.           " popis="O-xylosyl/N-acetylgalactosaminylglycan synthesis deficiencies" plati_od="2016-01-01" />
  <VETA kod="9.2.3.1.         " popis="SLC35D1 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.2.4.           " popis="O-mannosylglycan synthesis deficiencies" plati_od="2016-01-01" />
  <VETA kod="9.2.4.1.         " popis="Protein-O-mannosyltransferase 1 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.2.4.2.         " popis="Protein-O-mannosyltransferase 2 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.2.4.3.         " popis="Protein-O-mannose beta-1,2-N-acetyglucosaminyltransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="9.2.4.4.         " popis="Fukutin deficiency" plati_od="2016-01-01" />
  <VETA kod="9.2.4.5.         " popis="Fukutin-related protein deficiency" plati_od="2016-01-01" />
  <VETA kod="9.2.4.6.         " popis="N-acetylglucosaminyltransferase-like protein deficiency" plati_od="2016-01-01" />
  <VETA kod="9.2.4.7.         " popis="O-fucose-specific beta-1,3-N-acetylglucosaminyltransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="9.2.4.8.         " popis="O-fucose-specific beta-1,3-N-glucosyltransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="9.3.             " popis="Disorders of glycosphingolipid and glycosylphosphatidylinositol anchor glycosylation" plati_od="2016-01-01" />
  <VETA kod="9.3.1.1.         " popis="Lactosylceramide alpha-2,3-sialyltransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="9.3.1.2.         " popis="Phosphatidylinositolglycan, class M deficiency" plati_od="2016-01-01" />
  <VETA kod="9.4.             " popis="Disorders of multiple glycosylation and other glycosylation pathways" plati_od="2016-01-01" />
  <VETA kod="9.4.1.           " popis="GDP-Man:Dol-P mannosyltransferase deficiency" plati_od="2016-01-01" />
  <VETA kod="9.4.2.           " popis="Lec35 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.4.3.           " popis="Beta-1,4-galactosyltransferase 1 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.4.4.           " popis="UDP-GlcNAc epimerase/kinase deficiency" plati_od="2016-01-01" />
  <VETA kod="9.4.5.           " popis="CMP-sialic acid transporter deficiency" plati_od="2016-01-01" />
  <VETA kod="9.4.6.           " popis="GDP-fucose transporter deficiency" plati_od="2016-01-01" />
  <VETA kod="9.4.7.           " popis="Dolichol pathway deficiencies" plati_od="2016-01-01" />
  <VETA kod="9.4.7.1.         " popis="Dolichol kinase deficiency" plati_od="2016-01-01" />
  <VETA kod="9.4.8.           " popis="Conserved oligomeric Golgi (COG) complex deficiency" plati_od="2016-01-01" />
  <VETA kod="9.4.8.1.         " popis="Component of COG complex 7 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.4.8.2.         " popis="Component of COG complex 1 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.4.8.3.         " popis="Component of COG complex 8 deficiency" plati_od="2016-01-01" />
  <VETA kod="9.4.9.           " popis="V-ATPase deficiencies" plati_od="2016-01-01" />
  <VETA kod="9.4.9.1.         " popis="V0 subunit A2 of vesicular H(+)-ATPase deficiency" plati_od="2016-01-01" />
  <VETA kod="9.5.             " popis="Disorders of protein ubiquitinylation" plati_od="2016-01-01" />
  <VETA kod="9.6.             " popis="Other disorders of protein modification" plati_od="2016-01-01" />
  <VETA kod="10.              " popis="Lysosomal disorders" plati_od="2016-01-01" />
  <VETA kod="10.1.            " popis="Mucopolysaccharidoses" plati_od="2016-01-01" />
  <VETA kod="10.1.1.          " popis="MPS I, Hurler, Scheie disease" plati_od="2016-01-01" />
  <VETA kod="10.1.2.          " popis="MPS II, Hunter disease" plati_od="2016-01-01" />
  <VETA kod="10.1.3.          " popis="MPS IIIA, Sanfilippo A disease" plati_od="2016-01-01" />
  <VETA kod="10.1.4.          " popis="MPS IIIB, Sanfilippo B disease" plati_od="2016-01-01" />
  <VETA kod="10.1.5.          " popis="MPS IIIC, Sanfilippo C disease" plati_od="2016-01-01" />
  <VETA kod="10.1.6.          " popis="MPS IIID, Sanfilippo D disease" plati_od="2016-01-01" />
  <VETA kod="10.1.7.          " popis="MPS IVA, Morquio A disease" plati_od="2016-01-01" />
  <VETA kod="10.1.8.          " popis="MPS IVB, Morquio B disease" plati_od="2016-01-01" />
  <VETA kod="10.1.9.          " popis="MPS VI, Maroteaux - Lamy disease" plati_od="2016-01-01" />
  <VETA kod="10.1.10.         " popis="MPS VII, Sly disease" plati_od="2016-01-01" />
  <VETA kod="10.1.11.         " popis="MPS IX" plati_od="2016-01-01" />
  <VETA kod="10.2.            " popis="Oligosaccharidoses" plati_od="2016-01-01" />
  <VETA kod="10.2.1.          " popis="Aspartylglucosaminuria" plati_od="2016-01-01" />
  <VETA kod="10.2.2.          " popis="Fucosidosis" plati_od="2016-01-01" />
  <VETA kod="10.2.3.          " popis="Alpha - D – mannosidosis" plati_od="2016-01-01" />
  <VETA kod="10.2.4.          " popis="Beta - D – mannosidosis" plati_od="2016-01-01" />
  <VETA kod="10.2.5.          " popis="Schindler disease" plati_od="2016-01-01" />
  <VETA kod="10.2.5.1.        " popis="Schindler disease type I" plati_od="2016-01-01" />
  <VETA kod="10.2.5.2.        " popis="Kanzaki disease" plati_od="2016-01-01" />
  <VETA kod="10.2.6.          " popis="Sialidosis" plati_od="2016-01-01" />
  <VETA kod="10.3.            " popis="Sphingolipidoses" plati_od="2016-01-01" />
  <VETA kod="10.3.1.          " popis="GM1-gangliosidosis" plati_od="2016-01-01" />
  <VETA kod="10.3.2.          " popis="GM2-gangliosidosis" plati_od="2016-01-01" />
  <VETA kod="10.3.2.1.        " popis="GM2-gangliosidosis 0-variant," plati_od="2016-01-01" />
  <VETA kod="10.3.2.2.        " popis="GM2-gangliosidosis B-variant" plati_od="2016-01-01" />
  <VETA kod="10.3.2.3.        " popis="GM2-gangliosidosis AB-variant" plati_od="2016-01-01" />
  <VETA kod="10.3.3.          " popis="Gaucher disease" plati_od="2016-01-01" />
  <VETA kod="10.3.4.          " popis="Krabbe disease" plati_od="2016-01-01" />
  <VETA kod="10.3.5.          " popis="Metachromatic leukodystrophy" plati_od="2016-01-01" />
  <VETA kod="10.3.6.          " popis="Prosaposin deficiency" plati_od="2016-01-01" />
  <VETA kod="10.3.6.1.        " popis="Saposin A deficiency" plati_od="2016-01-01" />
  <VETA kod="10.3.6.2.        " popis="Saposin B deficiency" plati_od="2016-01-01" />
  <VETA kod="10.3.6.3.        " popis="Saposin C deficiency" plati_od="2016-01-01" />
  <VETA kod="10.3.6.4.        " popis="Saposin D deficiency" plati_od="2016-01-01" />
  <VETA kod="10.3.7.          " popis="Fabry disease" plati_od="2016-01-01" />
  <VETA kod="10.3.8.          " popis="Farber disease" plati_od="2016-01-01" />
  <VETA kod="10.3.9.          " popis="Niemann-Pick disease type A or B" plati_od="2016-01-01" />
  <VETA kod="10.3.10.         " popis="Niemann-Pick disease type C" plati_od="2016-01-01" />
  <VETA kod="10.3.10.1.       " popis="Niemann-Pick disease type C1" plati_od="2016-01-01" />
  <VETA kod="10.3.10.2.       " popis="Niemann-Pick disease type C2" plati_od="2016-01-01" />
  <VETA kod="10.4.            " popis="Ceroid lipfuscinoses, neuronal (CLN)" plati_od="2016-01-01" />
  <VETA kod="10.4.1.          " popis="CLN1, Santavuori-Haltia disease" plati_od="2016-01-01" />
  <VETA kod="10.4.2.          " popis="CLN2, Jansky-Bielschowsky disease" plati_od="2016-01-01" />
  <VETA kod="10.4.3.          " popis="CLN3, Batten Spielmeyer-Vogt disease" plati_od="2016-01-01" />
  <VETA kod="10.4.4.          " popis="CLN4A, Kufs disease recessive type" plati_od="2016-01-01" />
  <VETA kod="10.4.5.          " popis="CLN4B Kufs disease dominant type" plati_od="2016-01-01" />
  <VETA kod="10.4.6.          " popis="CLN5 Finnish variant" plati_od="2016-01-01" />
  <VETA kod="10.4.7.          " popis="CLN6" plati_od="2016-01-01" />
  <VETA kod="10.4.8.          " popis="CLN7" plati_od="2016-01-01" />
  <VETA kod="10.4.9.          " popis="CLN8, Northern epilepsy type" plati_od="2016-01-01" />
  <VETA kod="10.4.10.         " popis="CLN9" plati_od="2016-01-01" />
  <VETA kod="10.4.11.         " popis="CLN10" plati_od="2016-01-01" />
  <VETA kod="10.5.            " popis="Lysosomal export disorders" plati_od="2016-01-01" />
  <VETA kod="10.5.1.          " popis="Cystinosis" plati_od="2016-01-01" />
  <VETA kod="10.5.2.          " popis="Salla disease/infantile sialic acid storage disease" plati_od="2016-01-01" />
  <VETA kod="10.6.            " popis="Other lysosomal disorders" plati_od="2016-01-01" />
  <VETA kod="10.6.1.          " popis="Mucolipidosis II, I-cell disease" plati_od="2016-01-01" />
  <VETA kod="10.6.2.          " popis="Mucolipidosis III, Pseudo-Hurler polydystrophy" plati_od="2016-01-01" />
  <VETA kod="10.6.3.          " popis="Mucolipidosis IV" plati_od="2016-01-01" />
  <VETA kod="10.6.4.          " popis="Multiple sulphatase deficiency" plati_od="2016-01-01" />
  <VETA kod="10.6.5.          " popis="Wolman/cholesterol ester storage disease" plati_od="2016-01-01" />
  <VETA kod="10.6.6.          " popis="Pompe disease, GSD type II" plati_od="2016-01-01" />
  <VETA kod="10.6.7.          " popis="Sialuria" plati_od="2016-01-01" />
  <VETA kod="10.6.8.          " popis="Danon disease" plati_od="2016-01-01" />
  <VETA kod="10.6.9.          " popis="Cathepsin-related disorders" plati_od="2016-01-01" />
  <VETA kod="10.6.9.1.        " popis="Galactosialidosis" plati_od="2016-01-01" />
  <VETA kod="10.6.9.2.        " popis="Papillon-Lefevre  syndrome" plati_od="2016-01-01" />
  <VETA kod="10.6.9.3.        " popis="Pycnodysostosis" plati_od="2016-01-01" />
  <VETA kod="10.6.10.         " popis="Hermansky-Pudlak Syndrome" plati_od="2016-01-01" />
  <VETA kod="11.              " popis="Peroxisomal disorders" plati_od="2016-01-01" />
  <VETA kod="11.1.            " popis="Disorders of peroxisome biogenesis" plati_od="2016-01-01" />
  <VETA kod="11.1.1.          " popis="Zellweger spectrum disorder, severe form" plati_od="2016-01-01" />
  <VETA kod="11.1.2.          " popis="Zellweger spectrum disorder, attenuated form" plati_od="2016-01-01" />
  <VETA kod="11.1.2.1.        " popis="Neonatal adrenoleukodystrophy" plati_od="2016-01-01" />
  <VETA kod="11.1.2.2.        " popis="Infantile Refsum disease" plati_od="2016-01-01" />
  <VETA kod="11.1.3.          " popis="Zellweger  spectrum disorder, unclassified clinical severity" plati_od="2016-01-01" />
  <VETA kod="11.1.3.1.        " popis="PEX1 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.1.3.2.        " popis="PEX2 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.1.3.3.        " popis="PEX3 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.1.3.4.        " popis="PEX5 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.1.3.5.        " popis="PEX6 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.1.3.6.        " popis="PEX10 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.1.3.7.        " popis="PEX12 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.1.3.8.        " popis="PEX13 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.1.3.9.        " popis="PEX14 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.1.3.10.       " popis="PEX16 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.1.3.11.       " popis="PEX19 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.1.3.12.       " popis="PEX26 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.2.            " popis="Rhizomelic chondrodysplasia punctata" plati_od="2016-01-01" />
  <VETA kod="11.2.1.          " popis="Rhizomelic chondrodysplasia punctata type 1" plati_od="2016-01-01" />
  <VETA kod="11.2.2.          " popis="Rhizomelic chondrodysplasia punctata type 2" plati_od="2016-01-01" />
  <VETA kod="11.2.3.          " popis="Rhizomelic chondrodysplasia punctata type 3" plati_od="2016-01-01" />
  <VETA kod="11.3.            " popis="Disorders of peroxisomal alpha-, beta and omega-oxidation" plati_od="2016-01-01" />
  <VETA kod="11.3.1.          " popis="X-linked adrenoleukodystrophy" plati_od="2016-01-01" />
  <VETA kod="11.3.2.          " popis="Peroxisomal acyl-CoA oxidase 1 deficiency" plati_od="2016-01-01" />
  <VETA kod="11.3.3.          " popis="Peroxisomal D-bifunctional protein deficiency" plati_od="2016-01-01" />
  <VETA kod="11.3.4.          " popis="Sterol carrier protein deficiency" plati_od="2016-01-01" />
  <VETA kod="11.3.5.          " popis="Alpha-methylacyl-CoA racemase deficiency" plati_od="2016-01-01" />
  <VETA kod="11.3.6.          " popis="Refsum  disease" plati_od="2016-01-01" />
  <VETA kod="11.4.            " popis="Other peroxisomal disorders" plati_od="2016-01-01" />
  <VETA kod="11.4.1.          " popis="Primary hyperoxaluria type I" plati_od="2016-01-01" />
  <VETA kod="11.4.2.          " popis="Acatalasaemia" plati_od="2016-01-01" />
  <VETA kod="12.              " popis="Disorders of neurotransmitter metabolism" plati_od="2016-01-01" />
  <VETA kod="12.1.            " popis="Disorders in the metabolism of biogenic amines" plati_od="2016-01-01" />
  <VETA kod="12.1.1.          " popis="Tyrosine hydroxylase deficiency" plati_od="2016-01-01" />
  <VETA kod="12.1.2.          " popis="Aromatic L-amino acid decarboxylase deficiency" plati_od="2016-01-01" />
  <VETA kod="12.1.3.          " popis="Dopamine beta-hydroxylase deficiency" plati_od="2016-01-01" />
  <VETA kod="12.2.            " popis="Disorders in the metabolism of gamma-aminobutyrate" plati_od="2016-01-01" />
  <VETA kod="12.2.1.          " popis="Succinic semialdehyde dehydrogenase deficiency" plati_od="2016-01-01" />
  <VETA kod="12.2.2.          " popis="GABA transaminase deficiency" plati_od="2016-01-01" />
  <VETA kod="12.3.            " popis="Other disorders of neurotransmitter metabolism" plati_od="2016-01-01" />
  <VETA kod="13.              " popis="Disorders in the metabolism of vitamins and (non-protein) cofactors" plati_od="2016-01-01" />
  <VETA kod="13.1.            " popis="Disorders of folate metabolism and transport" plati_od="2016-01-01" />
  <VETA kod="13.1.1.          " popis="Hereditary folate malabsorption" plati_od="2016-01-01" />
  <VETA kod="13.1.2.          " popis="Cerebral folate deficiency due to FOLR1 deficiency" plati_od="2016-01-01" />
  <VETA kod="13.1.3.          " popis="Methylenetetrahydrofolate reductase deficiency" plati_od="2016-01-01" />
  <VETA kod="13.1.4.          " popis="Other genetic disorders in folate transport and metabolism" plati_od="2016-01-01" />
  <VETA kod="13.1.5.          " popis="Unspecified disorders of folate transport and metabolism" plati_od="2016-01-01" />
  <VETA kod="13.1.6.          " popis="Secondary disorders of folate transport and metabolism" plati_od="2016-01-01" />
  <VETA kod="13.1.7.          " popis="Cerebral folate deficiency due to autoantibodies-non-genetic" plati_od="2016-01-01" />
  <VETA kod="13.2.            " popis="Disorders of cobalamin absorption, transport and metabolism" plati_od="2016-01-01" />
  <VETA kod="13.2.1.          " popis="Intrinsic factor deficiency" plati_od="2016-01-01" />
  <VETA kod="13.2.2.          " popis="Enterocyte intrinsic factor receptor deficiency" plati_od="2016-01-01" />
  <VETA kod="13.2.2.1.        " popis="Intrinsic factor receptor deficiency due to CUBN mutations" plati_od="2016-01-01" />
  <VETA kod="13.2.2.2.        " popis="Intrinsic factor receptor deficiency due to AMN mutations" plati_od="2016-01-01" />
  <VETA kod="13.2.3.          " popis="Haptocorrin deficiency" plati_od="2016-01-01" />
  <VETA kod="13.2.4.          " popis="Transcobalamin II deficiency" plati_od="2016-01-01" />
  <VETA kod="13.2.5.          " popis="Defect in adenosylcobalamin synthesis-cbl A" plati_od="2016-01-01" />
  <VETA kod="13.2.6.          " popis="Defect in adenosylcobalamin synthesis-cbl B" plati_od="2016-01-01" />
  <VETA kod="13.2.7.          " popis="Defect in adenosylcobalamin synthesis-cblD-MMA" plati_od="2016-01-01" />
  <VETA kod="13.2.8.          " popis="Defect in methylcobalamin synthesis-cblD-HC" plati_od="2016-01-01" />
  <VETA kod="13.2.9.          " popis="Combined defect in adenosylcobalamin and methylcobalamin synthesis-cblC" plati_od="2016-01-01" />
  <VETA kod="13.2.10.         " popis="Combined defect in adenosylcobalamin and methylcobalamin synthesis-cblD" plati_od="2016-01-01" />
  <VETA kod="13.2.11.         " popis="Combined defect in adenosylcobalamin and methylcobalamin synthesis-cblF" plati_od="2016-01-01" />
  <VETA kod="13.2.12.         " popis="Transcobalamin receptor (TCblR/CD320) defect" plati_od="2016-01-01" />
  <VETA kod="13.2.13.         " popis="Other genetic defect in cobalamin transport and metabolism" plati_od="2016-01-01" />
  <VETA kod="13.2.14.         " popis="Unspecified disorder of cobalamin absorption, transport and metabolism" plati_od="2016-01-01" />
  <VETA kod="13.2.15.         " popis="Secondary non-genetic disorders of cobalamin absorption, transport and metabolism" plati_od="2016-01-01" />
  <VETA kod="13.3.            " popis="Disorders of pterin metabolism" plati_od="2016-01-01" />
  <VETA kod="13.3.1.          " popis="Guanosine 5 triphosphate cyclohydrolase I deficiency" plati_od="2016-01-01" />
  <VETA kod="13.3.2.          " popis="6-Pyruvoyl-tetrahydropterin synthase deficiency" plati_od="2016-01-01" />
  <VETA kod="13.3.3.          " popis="Sepiapterin reductase deficiency" plati_od="2016-01-01" />
  <VETA kod="13.3.4.          " popis="Quinoid dihydropteridine reductase deficiency" plati_od="2016-01-01" />
  <VETA kod="13.3.5.          " popis="Pterin 4 carbinolamine dehydratase deficiency" plati_od="2016-01-01" />
  <VETA kod="13.4.            " popis="Disorders of vitamin D metabolism and transport" plati_od="2016-01-01" />
  <VETA kod="13.5.            " popis="Disorders of biotin metabolism" plati_od="2016-01-01" />
  <VETA kod="13.5.1.          " popis="Biotinidase deficiency" plati_od="2016-01-01" />
  <VETA kod="13.5.2.          " popis="Holocarboxylase synthetase deficiency" plati_od="2016-01-01" />
  <VETA kod="13.6.            " popis="Disorders of pyridoxine metabolism" plati_od="2016-01-01" />
  <VETA kod="13.6.1.          " popis="Pyridoxine-dependent seizures" plati_od="2016-01-01" />
  <VETA kod="13.6.2.          " popis="Pyridoxamine 5´-oxidase deficiency" plati_od="2016-01-01" />
  <VETA kod="13.7.            " popis="Disorders of thiamine metabolism" plati_od="2016-01-01" />
  <VETA kod="13.7.1.          " popis="Thiamine-responsive megaloblastic anemia syndrome" plati_od="2016-01-01" />
  <VETA kod="13.7.2.          " popis="Biotin-responsive basal ganglia disease" plati_od="2016-01-01" />
  <VETA kod="13.7.3.          " popis="Microcephaly, Amish type" plati_od="2016-01-01" />
  <VETA kod="13.8.            " popis="Disorders of molybdenum cofactor metabolism" plati_od="2016-01-01" />
  <VETA kod="13.8.1.          " popis="Molybdenum cofactor deficiency" plati_od="2016-01-01" />
  <VETA kod="13.8.1.1.        " popis="Mo cofactor deficiency, complementation group A" plati_od="2016-01-01" />
  <VETA kod="13.8.1.2.        " popis="Mo cofactor deficiency, complementation group B" plati_od="2016-01-01" />
  <VETA kod="13.8.1.3.        " popis="Mo cofactor deficiency, complementation group C" plati_od="2016-01-01" />
  <VETA kod="13.9.            " popis="Other disorders of vitamins and cofactors" plati_od="2016-01-01" />
  <VETA kod="13.9.1.          " popis="TTP1 deficiency" plati_od="2016-01-01" />
  <VETA kod="13.9.2.          " popis="Vitamin K epoxide reductase deficiency" plati_od="2016-01-01" />
  <VETA kod="13.9.3.          " popis="Retinol binding protein deficiency" plati_od="2016-01-01" />
  <VETA kod="13.9.4.          " popis="Pantothenate kinases deficiency" plati_od="2016-01-01" />
  <VETA kod="14.              " popis="Disorders in the metabolism of trace elements and metals" plati_od="2016-01-01" />
  <VETA kod="14.1.            " popis="Disorder of copper metabolism" plati_od="2016-01-01" />
  <VETA kod="14.1.1.          " popis="Menkes syndrome" plati_od="2016-01-01" />
  <VETA kod="14.1.2.          " popis="Occipital horn syndrome" plati_od="2016-01-01" />
  <VETA kod="14.1.3.          " popis="Wilson disease" plati_od="2016-01-01" />
  <VETA kod="14.2.            " popis="Disorder of iron metabolism" plati_od="2016-01-01" />
  <VETA kod="14.2.1.          " popis="Hereditary haemochromatosis" plati_od="2016-01-01" />
  <VETA kod="14.2.1.1.        " popis="Hereditary haemochromatosis Type 1" plati_od="2016-01-01" />
  <VETA kod="14.2.1.2.        " popis="Hereditary haemochromatosis Type 2" plati_od="2016-01-01" />
  <VETA kod="14.2.1.3.        " popis="Hereditary haemochromatosis Type 3" plati_od="2016-01-01" />
  <VETA kod="14.2.1.4.        " popis="Hereditary haemochromatosis Type 4" plati_od="2016-01-01" />
  <VETA kod="14.2.2.          " popis="Neonatal haemochromatosis" plati_od="2016-01-01" />
  <VETA kod="14.2.3.          " popis="Haemosiderosis, acquired" plati_od="2016-01-01" />
  <VETA kod="14.3.            " popis="Disorder of zinc metabolism" plati_od="2016-01-01" />
  <VETA kod="14.3.1.          " popis="Acrodermatitis enteropathica" plati_od="2016-01-01" />
  <VETA kod="14.3.2.          " popis="Hyperzincemia and hypercalprotectinemia" plati_od="2016-01-01" />
  <VETA kod="14.4.            " popis="Disorder of phosphate, calcium and vitamin D metabolism" plati_od="2016-01-01" />
  <VETA kod="14.5.            " popis="Disorder of magnesium metabolism" plati_od="2016-01-01" />
  <VETA kod="14.5.1.          " popis="Hypermagnesaemia" plati_od="2016-01-01" />
  <VETA kod="14.5.2.          " popis="Hypomagnesaemia" plati_od="2016-01-01" />
  <VETA kod="14.5.3.          " popis="Primary hypomagnesaemia" plati_od="2016-01-01" />
  <VETA kod="14.5.3.1.        " popis="Isolated familial renal hypomagnesaemia" plati_od="2016-01-01" />
  <VETA kod="14.5.3.2.        " popis="Familial hypokalaemia - hypomagnesaemia" plati_od="2016-01-01" />
  <VETA kod="14.5.3.3.        " popis="Familial hypomagnesaemia - hypercalciuria" plati_od="2016-01-01" />
  <VETA kod="14.5.3.4.        " popis="Isolated familial intestinal hypomagnesaemia" plati_od="2016-01-01" />
  <VETA kod="14.5.4.          " popis="Secondary hypomagnesaemia" plati_od="2016-01-01" />
  <VETA kod="14.5.4.1.        " popis="Neonatal hypomagnesaemia" plati_od="2016-01-01" />
  <VETA kod="14.5.4.2.        " popis="Hypomagnesaemic tetany in newborn" plati_od="2016-01-01" />
  <VETA kod="14.5.4.3.        " popis="Drug induced hypomagnesaemia" plati_od="2016-01-01" />
  <VETA kod="14.5.5.          " popis="Hypomagnesaemic tetany" plati_od="2016-01-01" />
  <VETA kod="14.6.            " popis="Disorders in the metabolism of other trace elements and metals" plati_od="2016-01-01" />
  <VETA kod="15.              " popis="Disorders and variants in the metabolism of xenobiotics" plati_od="2016-01-01" />
  <VETA kod="15.1.            " popis="Disorders and variants of cytochrome P450-mediated oxidation" plati_od="2016-01-01" />
  <VETA kod="15.2.            " popis="Disorders and variants of other enzymes that oxidise xenobiotics" plati_od="2016-01-01" />
  <VETA kod="15.2.1.          " popis="Trimethylaminuria" plati_od="2016-01-01" />
  <VETA kod="15.3.            " popis="Disorders and variants of xenobiotics conjugation" plati_od="2016-01-01" />
  <VETA kod="15.4.            " popis="Disorders and variants of xenobiotics transport" plati_od="2016-01-01" />
  <VETA kod="99.              " popis="Others" plati_od="2016-01-01" />
  <VETA kod="99.1.            " popis="CADASIL" plati_od="2016-01-01" />
</ciselnik>