"Coupling state"
11beta-hydroxysteroid dehydrogenáza (typ II)
2,3-bisfosfoglycerát: vazba na hemoglobin
2-metyl-3-hydroxybutyryl-CoA dehydrogenázy deficit
2-metylbutyryl-CoA dehydrogenázy deficit
DH komplexu (nespecif.) deficit
2. věta termodynamická (Carnotův cyklus)
252Cf
3-fosfo-D-glycerát 1,2-fosfomutáza
3-hydroxy-2-metylbutyryl-CoA dehydrogenáza
3-hydroxy-3-metylglutarová acidurie
3-hydroxy-3-metylglutaryl-CoA syntáza: deficit
3-hydroxybutanoátdehydrogenáza
3-hydroxyisobutyryl-CoA hydroláza
3-hydroxyizobutyryl-CoA deacylázy deficit
3-metyl-2-oxobutanoát dehydrogenáza
3-metylglutakonová acidurie typu IV
3-metylkrotonyl-CoA
3-oxopristanoyl-CoA
3beta-hydroxysteroid-D24-reduktáza: deficit
3beta-hydroxysteroid-dehydrogenázy deficit
3beta-hydroxysteroid-isomerázy deficit
4-hydroxyfenylpyruvát dioxygenáza
4-oxoprolin reduktáza (Hydroxyprolinoxidáza)
4a-hydroxytetrahydrobiopterin dehydratáza
5,10-methylentetrahydrofolát reduktáza (FADH)
6-pyruvoyltetrahydropterin syntáza